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Table 1 Phenotypic characterization of MSCs and OBs from a PPRD patient and normal subjects

From: Mesenchymal stromal cells from a progressive pseudorheumatoid dysplasia patient show altered osteogenic differentiation

Markers

PPRD MSC %

Normal MSC % median (range)

PPRD osteoblasts

%

Normal osteoblasts % median (range)

CD34

0

1 (1–2)

2

2 (1–2)

CD105

100

98 (94–100)

100

98 (45–100)

CD146

4

30 (15–37)

27

2 (1–9)

Collagen type I

88

79 (35–100)

96

36 (4–94)

OC

60

87 (75–95)

100

53 (6–81)

BSP

17

40 (29–83)

25

24 (3–90)

AP

9

5 (1–29)

14

22 (2–38)

  1. PPRD markers out of normal range are indicated in bold
  2. OC osteocalcin, BSP bone sialoprotein, AP alkaline phosphatase